Scimitar syndrome is characterised by hypoplasia and anomalous pulmonary venous drainage of the right lung. Because of its rarity, we present a case of a 21 years old male who came with respiratory tract symptoms and pulmonary arterial hypertension and was diagnosed with Scimitar syndrome with unilobar right lung based on imaging methods and FOB findings.
Key words: Scimitars syndrome, pulmonary arterial hypertension, lung hypoplasia
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