Abstract

Abstract:
Myotonia congenital (MC) is a skeletal muscle disorder which may cause malignant hyperthermia.
We want to exhibit you, our anesthesia experience in a patient who suffer from MC in this article.
Case
A 54-year-old male patient with right upper quadrant abdominal pain admitted to a general surgery clinic for cholecystectomy. The patient was diagnosed with MC at the age of 16 with complaints of fatigue and was followed by oral treatment of carbamazepin 200 mg per day. Because of the precautions of malignant hyperthermia and opioid based anesthesia, the patient was discharged to the general surgery ward with full recovery .
Discussion
In MC patiens, preoperative evaluation, laboratory tests, relevant consultations, anesthetic drugs to be used, normothermia and ICU follow-up in postoperative period are important.

Key words: MYOTONIA KONGENITA, TIVA, ANESTHESIA