Abstract

Background: Studies of adrenocortical carcinoma is an aggressive rare type of endocrine tumors. It possesses a high mortality rate. This type of carcinomas occurs sporadically, while it could be part of hereditary syndromes. Only limited data is found about the recurrence of these tumors after resection and their prognosis is unclear.
Case Presentation: We present a case of a four-year-old boy who presented with virilization symptoms and was referred for further investigation of left abdominal mass. He was cushingoid upon examination. The patient was managed by left nephrectomy and chemotherapy. Upon follow up, the residual mass lesion was seen on CT. Re-resection of the residual tumor was done. Adjuvant mitotane therapy and radiotherapy were started, 7 months later the patient was discovered to have left lung metastasis in which he underwent left lung wedge resection.

Key words: Adrenocortical tumors, adrenocortical carcinoma, lung metastasis.