Persistent left superior vena cava accompanied by an absent right superior vena cava in visceroatrial situs solitus is an extremely rare congenital anomaly. Although absence of RSVC alone in patients with visceroatrial situs solitus is of no hemodynamic significance, its diagnosis before surgery or other invasive procedure is important to avoid various management difficulties, which include complications such as the implantation of a transvenous pacemaker or defibrillator, placement of pulmonary artery catheter for intraoperative or intensive care unit monitoring, systemic venous cannulation for cardiopulmonary bypass or extracorporeal circulation, cavopulmonary anastomosis, and orthtopic heart transplantation. We present a case with the absence of RSVC along with PLSVC in association with a discrete subaortic membrane, at the end of which the patient was operated successfully.
Key Words: Superior Vena Cava; Systemic Venous Return Anomaly; Discrete Subaortic Stenosis; Cardiovascular Surgery.
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