Low-grade fibromyxoid sarcoma (LGFMS) is a rare adult mesenchymal tumor located mostly in deep soft tissues, which is not common in the pediatric patients. Only 20% of reported cases show patients under the age of 18. A systematic literature review of articles between 1995 and 2013 in MEDLINE and PubMed shows that fewer than 10 fibromyxoid sarcoma have thus far been identified in childhood. In this report authors describe a case of low-grade fibromyxoid sarcoma in the right arm of a 3-year-old girl. The tumor was excised with preservation of nearby neural structures, there was no functional deficit in arm functions and in follow-ups no recurrences have been seen so far. To the best of our knowledge, this is the youngest case of low-grade fibromyxoid sarcoma.
Key words: Low-grade fibromyxoid sarcoma, childhood, axillary nerve, soft tissue tumor
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