Abstract

Background: Ewing's family tumors are malignant and occur in children and young adults.Sinonasal region is slightly rare in occurrence and can present in various types of symptomatology .Ewing sarcoma (ES) and primitive neuro-ectodermal tumor(PNET) are the most common entities in this family. The preliminary diagnosis is always confused because of delayed symptoms and improper histopathological and immunohistochemistry (IHC). Most of the complaints are because of tumor mass pressing and displacing the neighboring structures. Case presentation: 36-years old male adult reported with progressively increasing face swelling on the bridge of the nose and forehead predominately on left side of three years duration. There was pain and blocking of left side nose first and then on the other side. There were also off and on episodes of epistaxis. Ultrasonography (US) and color flow imaging (CFI) confirmed the swelling of solid consistency with hypervascularity. The patient underwent CECT and MRI studies which delineated the entity and was confirmed by histopathology. Conclusion: Sino nasal masses require detailed cross sectional imaging studies, histopathological and immunohistochemistry confirmation for proper and in time management strategies.

Key words: Ewing's family; PNET; immunohistochemistry; CFI; CECT; MRI.