Abstract

Oromandibular limb hypogenesis syndrome (OLHS) is a rare congenital disorder with only a handful of cases reported worldwide. Isolated hypoglossia/microglossia is rarer, with very few cases presenting for surgical procedures requiring anesthesia. This case reports the successful anesthesia management of a 5-year-old boy who presented for colostomy closure and had a previous history of difficult tracheal intubation.

Key words: hypoglossia; micrognathia; macroglossia; anesthesia; case report