Atypical presentations of Kawasaki’s disease have been described in the form of intestinal pseudo-obstruction,
tonsillitis, hemorrhagic serous effusions, thrombocytopenia, and non-fulfillment of all criteria for diagnosis of
Kawasaki’s disease. However, presentation of Kawasaki’s disease with shock and need for ionotropic support
have been rarely described. We present a 4-year-old girl with Kawasaki’s disease who presented with anasarca,
oliguria, shock, and presence of dilated coronary arteries within 5 days of fever and responded to intravenous
immunoglobulin (IVIG) and inotropic support.
Atypical presentation, children, Kawasaki’s disease